Preferred Label : Severe combined immunodeficiency T- B- due to adenosine deaminase deficiency;
ICD-11 definition : Severe combined immunodeficiency (SCID; ) due to adenosine deaminase (ADA) deficiency
is a form of SCID characterized by profound lymphopenia and very low immunoglobulin
levels of all isotypes resulting in severe and recurrent opportunistic infections.;
ICD-11 synonym : SCID T- B- due to adenosine deaminase deficiency; ADA - [adenosine aminohydrolase] deficiency; ADA - [adenosine deaminase] deficiency; ADA deficiency; SCID - [severe combined immunodeficiency] T- B- due to adenosine deaminase deficiency; Adenosine deaminase deficiency;
Severe combined immunodeficiency (SCID; ) due to adenosine deaminase (ADA) deficiency
is a form of SCID characterized by profound lymphopenia and very low immunoglobulin
levels of all isotypes resulting in severe and recurrent opportunistic infections.