Preferred Label : Pilar leiomyoma;
ICD-11 definition : Pilar leiomyoma is a benign cutaneous tumour derived from the arrector pili muscle
of the pilosebaceous follicle. Solitary lesions may develop anywhere on hair-bearing
skin, particularly the trunk and limbs. Multiple lesions have a predilection for the
face, back and extensor surfaces of the extremities and are often painful. Multiple
pilar leiomyomata may be familial with autosomal dominant inheritance and associated
with uterine leiomyomata in women, and, in some pedigrees, renal carcinoma (HLRCC;
Hereditary leiomyomatosis with renal cell cancer).;
ICD-11 synonym : Cutaneous leiomyoma; Piloleiomyoma;
Origin ID : 2131740285;
Automatic exact mappings (from CISMeF team)
Pilar leiomyoma is a benign cutaneous tumour derived from the arrector pili muscle
of the pilosebaceous follicle. Solitary lesions may develop anywhere on hair-bearing
skin, particularly the trunk and limbs. Multiple lesions have a predilection for the
face, back and extensor surfaces of the extremities and are often painful. Multiple
pilar leiomyomata may be familial with autosomal dominant inheritance and associated
with uterine leiomyomata in women, and, in some pedigrees, renal carcinoma (HLRCC;
Hereditary leiomyomatosis with renal cell cancer).
