Preferred Label : Familial multiple café-au-lait macules;
ICD-11 definition : Neurofibromatosis type 6 (NF6), also referred as café-au-lait spots syndrome, is a
cutaneous disorder characterized by the presence of several café-au-lait macules without
any other manifestations of neurofibromatosis or any other systemic disorder.;
ICD-11 synonym : Neurofibromatosis type 6; NF6 - [Neurofibromatosis type 6]; Café-au-lait spots syndrome;
ICD-11 acronym : NF6;
Origin ID : 2112681823;
Automatic exact mappings (from CISMeF team)
Neurofibromatosis type 6 (NF6), also referred as café-au-lait spots syndrome, is a
cutaneous disorder characterized by the presence of several café-au-lait macules without
any other manifestations of neurofibromatosis or any other systemic disorder.