Preferred Label : Cogan syndrome;
ICD-11 definition : Vasculitis occurring in patients with Cogan's syndrome. Cogan's syndrome is characterized
by ocular inflammatory lesions, including interstitial keratitis, uveitis, and episcleritis,
and inner ear disease, including sensorineural hearing loss and vestibular dysfunction.
Vasculitic manifestations may include arteritis (affecting small, medium or large
arteries), aortitis, aortic aneurysms, and aortic and mitral valvulitis.;
Origin ID : 2098089327;
Automatic exact mappings (from CISMeF team)
Vasculitis occurring in patients with Cogan's syndrome. Cogan's syndrome is characterized
by ocular inflammatory lesions, including interstitial keratitis, uveitis, and episcleritis,
and inner ear disease, including sensorineural hearing loss and vestibular dysfunction.
Vasculitic manifestations may include arteritis (affecting small, medium or large
arteries), aortitis, aortic aneurysms, and aortic and mitral valvulitis.