Preferred Label : Right ventricular hypoplasia;
ICD-11 definition : A congenital cardiovascular malformation in which the right ventricle is abnormally
small (below the lower limit of normal adjusted for body size). This morphological
abnormality usually is an integral part of other congenital cardiovascular anomalies
and, therefore, frequently does not need to be coded separately. It should, however,
be coded as secondary to an accompanying congenital cardiovascular anomaly if the
right ventricular hypoplasia is not considered an integral and understood part of
the primary congenital cardiovascular diagnosis. It would rarely be coded as a primary
and/or isolated diagnosis.;
ICD-11 synonym : Hypoplastic right ventricle;
Origin ID : 2088837187;
Automatic exact mappings (from CISMeF team)
A congenital cardiovascular malformation in which the right ventricle is abnormally
small (below the lower limit of normal adjusted for body size). This morphological
abnormality usually is an integral part of other congenital cardiovascular anomalies
and, therefore, frequently does not need to be coded separately. It should, however,
be coded as secondary to an accompanying congenital cardiovascular anomaly if the
right ventricular hypoplasia is not considered an integral and understood part of
the primary congenital cardiovascular diagnosis. It would rarely be coded as a primary
and/or isolated diagnosis.
