Preferred Label : Histiocytic necrotising lymphadenitis of Kikuchi and Fujimoto;
ICD-11 definition : Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign,
self-limited but poorly understood disease characterised by malaise, fever, weight
loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other
important features found in a minority of cases include lymphocytopenia, a variety
of skin manifestations and an association with systemic lupus erythematosus. The histological
hallmark is histiocytic infiltration and necrosis of lymph nodes.;
ICD-11 synonym : Kikuchi-Fujimoto disease;
Origin ID : 2087666237;
Automatic exact mappings (from CISMeF team)
Histiocytic necrotizing lymphadenitis (Kikuchi-Fujimoto disease) is a rare benign,
self-limited but poorly understood disease characterised by malaise, fever, weight
loss and localised lymphadenopathy affecting particularly cervical lymph nodes. Other
important features found in a minority of cases include lymphocytopenia, a variety
of skin manifestations and an association with systemic lupus erythematosus. The histological
hallmark is histiocytic infiltration and necrosis of lymph nodes.
