Preferred Label : Steatocystoma multiplex;
ICD-11 definition : Steatocystoma multiplex is a rare autosomal dominant genodermatosis characterized
by the development of multiple intradermal cysts with sebaceous gland lobules in their
wall and sebum in their lumen. It usually first manifests in adolescence or early
adult life with multiple smooth compressible dermal nodules involving the trunk, particularly
the presternal area, and proximal limbs. Suppuration and scarring commonly occur.;
ICD-11 synonym : sebocystomatosis;
Origin ID : 2085770731;
Automatic exact mappings (from CISMeF team)
Steatocystoma multiplex is a rare autosomal dominant genodermatosis characterized
by the development of multiple intradermal cysts with sebaceous gland lobules in their
wall and sebum in their lumen. It usually first manifests in adolescence or early
adult life with multiple smooth compressible dermal nodules involving the trunk, particularly
the presternal area, and proximal limbs. Suppuration and scarring commonly occur.
