Preferred Label : Hereditary factor XIII deficiency;
ICD-11 definition : Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced
levels and activity of factor XIII and characterized by haemorrhagic diathesis frequently
associated with spontaneous abortions and defective wound healing. Factor XIII deficiency
is one of the most rare coagulation factor deficiencies. Both sexes are equally affected.;
ICD-11 inclusion : factor XIII deficiency disease; hereditary factor XIII deficiency disease; deficiency of factor XIII; deficiency of stable factor; congenital factor XIII deficiency;
Origin ID : 2079957863;
Automatic exact mappings (from CISMeF team)
Congenital factor XIII deficiency is an inherited bleeding disorder due to reduced
levels and activity of factor XIII and characterized by haemorrhagic diathesis frequently
associated with spontaneous abortions and defective wound healing. Factor XIII deficiency
is one of the most rare coagulation factor deficiencies. Both sexes are equally affected.
