Congenital pulmonary lymphangiectasia

Preferred Label : Congenital pulmonary lymphangiectasia;

ICD-11 definition : Congenital pulmonary lymphangiectasia is a rare developmental disorder involving the lung and characterized by pulmonary subpleural, interlobar, perivascular, and peribronchial lymphatic dilatation.;

ICD-11 synonym : Pulmonary lymphangiomatosis;

Details

Origin ID

2069435755;

Automatic exact mappings (from CISMeF team)
- Pulmonary lymphangiomatosis [PASCAL descriptor]
Currated CISMeF NLP mapping
- Congenital Pulmonary Lymphangiectasia [NCIt concept]
- Congenital pulmonary lymphangiectasia [ORDO Disease]
- Congenital pulmonary lymphangiectasis (disorder) [SNOMED CT concept]
- Lymphangiectasia, pulmonary, congenital [MeSH concept]
- Lymphangiectasia, pulmonary, congenital [OMIM Phenotype]
- Pulmonary lymphangiectasia, congenital [HPO term]
- congenital pulmonary lymphangiectasis [SNOMED Notion]
- lymphangiectasia, pulmonary, congenital [MeSH Supplementary Concept]

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