Preferred Label : Kasabach-Merritt syndrome;
ICD-11 definition : Kasabach-Merritt syndrome is characterised by the association of a vascular tumour
with severe thrombopaenia and various degrees of consumption coagulopathy (most commonly
marked by decreased levels of fibrinogen, presence of elevated levels of soluble complexes,
and very high levels of D-dimers).;
Origin ID : 2059601885;
Automatic exact mappings (from CISMeF team)
Kasabach-Merritt syndrome is characterised by the association of a vascular tumour
with severe thrombopaenia and various degrees of consumption coagulopathy (most commonly
marked by decreased levels of fibrinogen, presence of elevated levels of soluble complexes,
and very high levels of D-dimers).