Preferred Label : Adult-onset leukodystrophy with axonal spheroids;
ICD-11 definition : These are familial or sporadic disorders of adult onset characterized by cerebral
white matter degeneration including myelin and axonal loss, gliosis, macrophages and
axonal spheroids.;
ICD-11 synonym : hereditary diffuse leukoencephalopathy with axonal spheroids;
Origin ID : 2040572438;
Automatic exact mappings (from CISMeF team)
These are familial or sporadic disorders of adult onset characterized by cerebral
white matter degeneration including myelin and axonal loss, gliosis, macrophages and
axonal spheroids.