" /> Familial cold autoinflammatory syndrome - CISMeF





Preferred Label : Familial cold autoinflammatory syndrome;

ICD-11 definition : Familial cold urticaria is an autosomal dominant autoinflammatory syndrome characterized by episodes of rash, fever, and joint pain following generalized exposure to cold.;

ICD-11 synonym : Familial cold urticaria;

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Familial cold urticaria is an autosomal dominant autoinflammatory syndrome characterized by episodes of rash, fever, and joint pain following generalized exposure to cold.

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28/07/2025


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