Preferred Label : Generalised morphoea;
ICD-11 definition : A rare disabling and potentially fatal condition in which diffuse symmetrical sclerosis
of the skin develops insidiously in the absence of associated systemic disturbances
or Raynaud phenomenon. The aetiology is unknown. Its onset is usually in early to
middle adult life, starting with plaques on the trunk which become confluent and then
spread to limbs, neck and head. It may impede breathing because of restriction of
thoracic wall movement.;
ICD-11 synonym : generalised scleroderma;
Origin ID : 1911879877;
Automatic exact mappings (from CISMeF team)
A rare disabling and potentially fatal condition in which diffuse symmetrical sclerosis
of the skin develops insidiously in the absence of associated systemic disturbances
or Raynaud phenomenon. The aetiology is unknown. Its onset is usually in early to
middle adult life, starting with plaques on the trunk which become confluent and then
spread to limbs, neck and head. It may impede breathing because of restriction of
thoracic wall movement.
