Sinus histiocytosis with massive lymphadenopathy

Preferred Label : Sinus histiocytosis with massive lymphadenopathy;

ICD-11 definition : This is a rare disorder of unknown etiology that is characterized by abundant histiocytes in the lymph nodes throughout the body.;

ICD-11 synonym : Rosai-Dorfman disease;

ICD-11 inclusion : Rosai-Dorfman disease;

Details

Origin ID

1908538383;

Automatic exact mappings (from CISMeF team)
- Histiocytosis-lymphadenopathy plus syndrome [OMIM Phenotype]
- Other histiocytosis syndromes [ICD-10 Sub-category]
- Rosai Dorfman disease [PASCAL descriptor]
- Rosai-Dorfman disease [Radlex concept]
- histiocytosis, sinus [MeSH Descriptor]
- histiocytosis-lymphadenopathy plus syndrome [DO Concept]
Currated CISMeF NLP mapping
- Rosai-Dorfman syndrome [MedDRA Preferred Term]
- Rosai-Dorfman-Destombes Disease [NCIt concept]
- Rosaï-Dorfman disease [ORDO Disease]
- Sinus histiocytosis with massive lymphadenopathy (disorder) [SNOMED CT concept]
- sinus histiocytosis with massive lymphadenopathy [SNOMED Notion]

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