" /> Common variable immunodeficiency - CISMeF





Preferred Label : Common variable immunodeficiency;

ICD-11 definition : Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases characterized by a significant hypogammaglobulinemia of unknown cause, failure to produce specific antibodies after immunizations and susceptibility to bacterial infections, predominantly caused by encapsulated bacteria.;

ICD-11 inclusion : CD19- [cluster of differentiation 40] deficiency; TACI - [transmembrane activator and calcium-modulating cyclophilin ligand interactor] deficiency; BAFF - [ B-cell activating factor] receptor deficiency; CD81 - [cluster of differentiation 81] deficiency; CD20 - [cluster of differentiation 20] deficiency; ICOS - [inducible costimulator] deficiency;

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Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases characterized by a significant hypogammaglobulinemia of unknown cause, failure to produce specific antibodies after immunizations and susceptibility to bacterial infections, predominantly caused by encapsulated bacteria.

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10/05/2025


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