Preferred Label : Common variable immunodeficiency;
ICD-11 definition : Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases
characterized by a significant hypogammaglobulinemia of unknown cause, failure to
produce specific antibodies after immunizations and susceptibility to bacterial infections,
predominantly caused by encapsulated bacteria.;
ICD-11 inclusion : CD19- [cluster of differentiation 40] deficiency; TACI - [transmembrane activator and calcium-modulating cyclophilin ligand interactor]
deficiency; BAFF - [ B-cell activating factor] receptor deficiency; CD81 - [cluster of differentiation 81] deficiency; CD20 - [cluster of differentiation 20] deficiency; ICOS - [inducible costimulator] deficiency;
Origin ID : 1908371517;
Currated CISMeF NLP mapping
Common variable immunodeficiency (CVID) comprises a heterogeneous group of diseases
characterized by a significant hypogammaglobulinemia of unknown cause, failure to
produce specific antibodies after immunizations and susceptibility to bacterial infections,
predominantly caused by encapsulated bacteria.