" /> Cantrell pentalogy - CISMeF





Preferred Label : Cantrell pentalogy;

ICD-11 definition : Cantrell pentalogy is a malformation syndrome of unknown etiology that consists of the following five features: midline supraumbilical abdominal wall defects; deficiency of the anterior diaphragm; defects in the diaphragmatic pericardium; defects of the lower sternum and congenital intracardiac defects, with exteriorisation of the heart, or 'ectopia cordis', being the most severe malformation.;

ICD-11 synonym : Cantrell syndrome; Pentalogy of Cantrell;

Details


Keyword's position in hierarchy(ies) : arborescence

You can consult :

Cantrell pentalogy is a malformation syndrome of unknown etiology that consists of the following five features: midline supraumbilical abdominal wall defects; deficiency of the anterior diaphragm; defects in the diaphragmatic pericardium; defects of the lower sternum and congenital intracardiac defects, with exteriorisation of the heart, or 'ectopia cordis', being the most severe malformation.

Nous contacter.
05/05/2025


[Home] [Top]

© Rouen University Hospital. Any partial or total use of this material must mention the source.