Preferred Label : Vogt-Koyanagi-Harada syndrome-associated anterior uveitis;
ICD-11 definition : A rare acquired inflammatory syndrome of unknown aetiology involving melanocyte-containing
tissues including the eye, inner ear, meninges, skin and hair. Clinical features include
bilateral chronic iridocyclitis and posterior uveitis; tinnitus and dysacusis; headache
and meningism; and poliosis, vitiligo and alopecia.;
ICD-11 synonym : Vogt-Koyanagi-Harada disease; VKH - [Vogt-Koyanagi-Harada syndrome]; Vogt-Koyanagi-Harada syndrome; Harada disease;
ICD-11 acronym : VKH;
Origin ID : 1883500946;
Automatic exact mappings (from CISMeF team)
Validated automatic mappings to NTBT
A rare acquired inflammatory syndrome of unknown aetiology involving melanocyte-containing
tissues including the eye, inner ear, meninges, skin and hair. Clinical features include
bilateral chronic iridocyclitis and posterior uveitis; tinnitus and dysacusis; headache
and meningism; and poliosis, vitiligo and alopecia.