Preferred Label : Von Willebrand disease type 1;
ICD-11 definition : Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterized
by a bleeding disorder associated with a partial quantitative plasmatic deficiency
of an otherwise structurally and functionally normal Willebrand factor (von Willebrand
factor; VWF). The type 1 disease is considered to be the most common form of VWD,
accounting for between 50 and 75% of cases but its prevalence is probably overestimated.
Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms
being associated with more severe VWF deficiency.;
Origin ID : 1861858008;
Automatic exact mappings (from CISMeF team)
Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterized
by a bleeding disorder associated with a partial quantitative plasmatic deficiency
of an otherwise structurally and functionally normal Willebrand factor (von Willebrand
factor; VWF). The type 1 disease is considered to be the most common form of VWD,
accounting for between 50 and 75% of cases but its prevalence is probably overestimated.
Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms
being associated with more severe VWF deficiency.
