Preferred Label : Congenital hydromyelia;
ICD-11 definition : A condition caused by failure of the spinal column to correctly develop during the
antenatal period. This condition is characterized by formation of a syrinx inside
the spinal cord cavity. This condition can also present with nerve deterioration due
to encroachment of the syrinx on the spinal cord.;
ICD-11 synonym : Hydrorachis;
ICD-11 inclusion : Hydromyelia; Hydrorachis;
Origin ID : 1842315334;
Automatic exact mappings (from CISMeF team)
A condition caused by failure of the spinal column to correctly develop during the
antenatal period. This condition is characterized by formation of a syrinx inside
the spinal cord cavity. This condition can also present with nerve deterioration due
to encroachment of the syrinx on the spinal cord.