Preferred Label : Benign concentric annular macular dystrophy;
ICD-11 definition : Benign concentric annular macular dystrophy (BCAMD) is a progressive autosomal dominant
macular dystrophy characterized by parafoveal hypopigmentation followed by a retinitis
pigmentosa-like phenotype (nyctalopia and peripheral vision loss) with a bull's eye
configuration.;
Origin ID : 1839503243;
Automatic exact mappings (from CISMeF team)
Benign concentric annular macular dystrophy (BCAMD) is a progressive autosomal dominant
macular dystrophy characterized by parafoveal hypopigmentation followed by a retinitis
pigmentosa-like phenotype (nyctalopia and peripheral vision loss) with a bull's eye
configuration.