" /> Chronic infantile neurological, cutaneous and articular syndrome - CISMeF





Preferred Label : Chronic infantile neurological, cutaneous and articular syndrome;

ICD-11 definition : Chronic Infantile Neurological, Cutaneous, and Articular (CINCA) syndrome is an autoinflammatory syndrome characterised by skin rash, joint involvement, chronic meningitis with granulocytes and, in some cases, sensorineural hearing loss and ocular signs.;

ICD-11 synonym : NOMID - [Neonatal-onset multisystem inflammatory disease]; CINCA syndrome; Prieur-Griscelli syndrome; IOMID - [Infantile-onset multisystem inflammatory disease]; Infantile-onset multisystem inflammatory disease; CINCA - [Chronic infantile neurological, cutaneous and articular] syndrome; Neonatal-onset multisystem inflammatory disease;

ICD-11 acronym : NOMID; IOMID; CINCA;

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Chronic Infantile Neurological, Cutaneous, and Articular (CINCA) syndrome is an autoinflammatory syndrome characterised by skin rash, joint involvement, chronic meningitis with granulocytes and, in some cases, sensorineural hearing loss and ocular signs.

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27/07/2025


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