Preferred Label : Endemic pemphigus foliaceus;
ICD-11 definition : Endemic pemphigus foliaceus is a chronic autoimmune skin diseases characterized by
superficial blister formation on the skin mediated by auto-antibodies to the desmosome
component desmoglein 1. Endemic pemphigus foliaceus has unique epidemiological features
of geographical, temporal and familial clustering.;
ICD-11 synonym : Fogo selvagem; Wild fire; Brazilian pemphigus;
Origin ID : 1681537638;
Automatic exact mappings (from CISMeF team)
Endemic pemphigus foliaceus is a chronic autoimmune skin diseases characterized by
superficial blister formation on the skin mediated by auto-antibodies to the desmosome
component desmoglein 1. Endemic pemphigus foliaceus has unique epidemiological features
of geographical, temporal and familial clustering.
