Preferred Label : Congenital pulmonary alveolar proteinosis;
ICD-11 definition : This is a primary, rare lung disease in which abnormal accumulation of surfactant
occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary
form or secondarily in the settings of malignancy (especially in myeloid leukemia),
pulmonary infection, or environmental exposure to dusts or chemicals.;
Origin ID : 1603032478;
Currated CISMeF NLP mapping
This is a primary, rare lung disease in which abnormal accumulation of surfactant
occurs within the alveoli, interfering with gas exchange. PAP can occur in a primary
form or secondarily in the settings of malignancy (especially in myeloid leukemia),
pulmonary infection, or environmental exposure to dusts or chemicals.
