Preferred Label : White sponge naevus;
ICD-11 definition : White sponge naevus is a rare and autosomal dominant genetic disease in which the
oral mucosa is white or greyish, thickened, folded, and spongy. The onset is early
in life, and both sexes are affected equally. Other common sites include the tongue,
floor of the mouth, and alveolar mucosa.;
ICD-11 synonym : Hereditary leukokeratosis of oral mucosa; Familial white folded mucosal dysplasia;
Origin ID : 1579656080;
Automatic exact mappings (from CISMeF team)
White sponge naevus is a rare and autosomal dominant genetic disease in which the
oral mucosa is white or greyish, thickened, folded, and spongy. The onset is early
in life, and both sexes are affected equally. Other common sites include the tongue,
floor of the mouth, and alveolar mucosa.
