ICD-11 definition : Acute intermittent porphyria is the most frequent and the most severe form of the
acute hepatic porphyrias. It is characterized by the occurrence of neuro-visceral
attacks without cutaneous manifestations.;
Acute intermittent porphyria is the most frequent and the most severe form of the
acute hepatic porphyrias. It is characterized by the occurrence of neuro-visceral
attacks without cutaneous manifestations.