Preferred Label : Atrichia with keratin cysts;
ICD-11 definition : Atrichia with papular lesions is a rare inherited form of alopecia characterized by
irreversible hair loss during the neonatal period on all hear-bearing areas of the
body, later associated with the development of papular lesions all over the body and
preferentially on the face and extensor surfaces of the extremities.;
ICD-11 synonym : Atrichia with papular lesions;
Origin ID : 155531758;
Automatic exact mappings (from CISMeF team)
Atrichia with papular lesions is a rare inherited form of alopecia characterized by
irreversible hair loss during the neonatal period on all hear-bearing areas of the
body, later associated with the development of papular lesions all over the body and
preferentially on the face and extensor surfaces of the extremities.
