Preferred Label : Pityriasis lichenoides et varioliformis acuta;
ICD-11 definition : Pityriasis lichenoides et varioliformis acuta, commonly referred to as PLEVA, is an
acute form of pityriasis lichenoides which manifests as crops of oedematous pink papules
over the proximal limbs and trunk which progress to vesicles and central haemorrhagic
necrosis before healing with scarring. The cause of PLEVA is unknown. It may be confused
clinically with varicella.;
ICD-11 synonym : Mucha-Habermann disease; PLEVA - [Pityriasis lichenoides et varioliformis acuta]; Pityriasis lichenoides acuta;
ICD-11 acronym : PLEVA;
Origin ID : 1545407981;
Automatic exact mappings (from CISMeF team)
Pityriasis lichenoides et varioliformis acuta, commonly referred to as PLEVA, is an
acute form of pityriasis lichenoides which manifests as crops of oedematous pink papules
over the proximal limbs and trunk which progress to vesicles and central haemorrhagic
necrosis before healing with scarring. The cause of PLEVA is unknown. It may be confused
clinically with varicella.