" /> Autosomal recessive polycystic kidney disease - CISMeF





Preferred Label : Autosomal recessive polycystic kidney disease;

ICD-11 definition : Autosomal recessive polycystic kidney disease (ARPKD) is an inherited condition characterised by multiple cysts affecting the collecting ducts giving rise to nephromegaly, arterial hypertension, urinary tract infection and chronic kidney disease (failure). Liver involvement (biliary abnormalities, cholangitis, portal hypertension) are frequently associated.;

ICD-11 synonym : infantile polycystic kidney disease; IPKD - [infantile polycystic kidney disease]; autosomal recessive polycystic kidney; ARPKD - [autosomal recessive polycystic kidney disease]; Polycystic kidney, infantile type; polycystic kidney disease, infantile type; multiple infantile type cyst of kidney; infantile type polycystic degeneration of kidney; autosomal recessive infantile polycystic kidney disease;

ICD-11 acronym : IPKD; ARPKD;

ICD-11 inclusion : Polycystic kidney, infantile type;

Détails


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Autosomal recessive polycystic kidney disease (ARPKD) is an inherited condition characterised by multiple cysts affecting the collecting ducts giving rise to nephromegaly, arterial hypertension, urinary tract infection and chronic kidney disease (failure). Liver involvement (biliary abnormalities, cholangitis, portal hypertension) are frequently associated.

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29/07/2025


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