Preferred Label : Reynolds syndrome;
ICD-11 definition : Reynolds syndrome is a rare autoimmune disease, consisting of the combination of primary
biliary cirrhosis and systemic sclerosis. In some patients this syndrome has also
been associated with Sjögren syndrome and haemolytic anemia. Typical clinical features
include jaundice, elevated blood levels of alkaline phosphatase, calcinosis cutis,
telangiectasia and pruritus.;
Origin ID : 1409844299;
Automatic exact mappings (from CISMeF team)
Reynolds syndrome is a rare autoimmune disease, consisting of the combination of primary
biliary cirrhosis and systemic sclerosis. In some patients this syndrome has also
been associated with Sjögren syndrome and haemolytic anemia. Typical clinical features
include jaundice, elevated blood levels of alkaline phosphatase, calcinosis cutis,
telangiectasia and pruritus.
