Preferred Label : Febrile ulceronecrotic Mucha-Habermann disease;
ICD-11 definition : Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant form of
pityriasis lichenoides et varioliformis (PLEVA) in which large necrotic cutaneous
lesions are accompanied by lymphadenopathy, general malaise, myalgia, neuropsychiatric
symptoms and high fever. Most cases occur in adults. As is the case with PLEVA, the
cause is unknown.;
ICD-11 synonym : FUNMH - [Febrile ulceronecrotic Mucha-Habermann disease];
ICD-11 acronym : FUNMH;
Origin ID : 1408299147;
Automatic exact mappings (from CISMeF team)
Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant form of
pityriasis lichenoides et varioliformis (PLEVA) in which large necrotic cutaneous
lesions are accompanied by lymphadenopathy, general malaise, myalgia, neuropsychiatric
symptoms and high fever. Most cases occur in adults. As is the case with PLEVA, the
cause is unknown.
