Preferred Label : Cutis marmorata telangiectatica congenita;
ICD-11 definition : Cutis marmorata telangiectatica congenita (CMTC) is a congenital localized or generalized
vascular anomaly characterized by a persistent cutis marmorata pattern with a marbled
bluish to deep purple appearance, spider nevus-like telangiectasia, phlebectasia and,
occasionally, ulceration and atrophy of the affected skin.;
ICD-11 synonym : Reticulate vascular naevus; Congenital phlebectasia; CMTC - [Cutis marmorata telangiectatica congenita];
ICD-11 acronym : CMTC;
ICD-11 inclusion : Reticulate vascular naevus; Congenital phlebectasia;
Origin ID : 1359154853;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Cutis marmorata telangiectatica congenita (CMTC) is a congenital localized or generalized
vascular anomaly characterized by a persistent cutis marmorata pattern with a marbled
bluish to deep purple appearance, spider nevus-like telangiectasia, phlebectasia and,
occasionally, ulceration and atrophy of the affected skin.