" /> Cutis marmorata telangiectatica congenita - CISMeF





Preferred Label : Cutis marmorata telangiectatica congenita;

ICD-11 definition : Cutis marmorata telangiectatica congenita (CMTC) is a congenital localized or generalized vascular anomaly characterized by a persistent cutis marmorata pattern with a marbled bluish to deep purple appearance, spider nevus-like telangiectasia, phlebectasia and, occasionally, ulceration and atrophy of the affected skin.;

ICD-11 synonym : Reticulate vascular naevus; Congenital phlebectasia; CMTC - [Cutis marmorata telangiectatica congenita];

ICD-11 acronym : CMTC;

ICD-11 inclusion : Reticulate vascular naevus; Congenital phlebectasia;

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Cutis marmorata telangiectatica congenita (CMTC) is a congenital localized or generalized vascular anomaly characterized by a persistent cutis marmorata pattern with a marbled bluish to deep purple appearance, spider nevus-like telangiectasia, phlebectasia and, occasionally, ulceration and atrophy of the affected skin.

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28/07/2025


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