Preferred Label : Gingival fibromatosis - hypertrichosis;
ICD-11 definition : Gingival fibromatosis - hypertrichosis is a rare autosomal dominant disorder characterized
by generalized enlargement of the gingivae occurring at birth or during childhood
that is associated with generalized hypertrichosis developping at birth, during the
first years of life, or even at puberty and prominently affecting the face, upper
limbs, and midback.;
ICD-11 synonym : Gingival fibromatosis-hypertrichosis syndrome;
Origin ID : 135845109;
Automatic exact mappings (from CISMeF team)
Gingival fibromatosis - hypertrichosis is a rare autosomal dominant disorder characterized
by generalized enlargement of the gingivae occurring at birth or during childhood
that is associated with generalized hypertrichosis developping at birth, during the
first years of life, or even at puberty and prominently affecting the face, upper
limbs, and midback.
