Preferred Label : Familial exudative vitreoretinopathy;
ICD-11 definition : Exudative vitreoretinopathy is a rare vitreoretinal dystrophy characterized by prematurely
interrupted blood vessel development in the peripheral retina. In its typical form,
large portions of avascular retina in the temporal periphery are associated with arteriovenous
anastomoses and neovascular proliferations around the ischaemic area, a peripheral
temporal fibrovascular mass, and a peculiar pattern of retinal vessels (vessels stretch
toward temporal periphery making an acute angle as they leave the optic disk).;
ICD-11 synonym : Criswick-Schepens syndrome; FEVR - [familial exudative vitreoretinopathy];
ICD-11 acronym : FEVR;
Origin ID : 1344358838;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Validated automatic mappings to BTNT
Exudative vitreoretinopathy is a rare vitreoretinal dystrophy characterized by prematurely
interrupted blood vessel development in the peripheral retina. In its typical form,
large portions of avascular retina in the temporal periphery are associated with arteriovenous
anastomoses and neovascular proliferations around the ischaemic area, a peripheral
temporal fibrovascular mass, and a peculiar pattern of retinal vessels (vessels stretch
toward temporal periphery making an acute angle as they leave the optic disk).