Preferred Label : Susac syndrome;
ICD-11 definition : Susac syndrome, also referred to as SICRET (Small Infarctions of Cochlear, Retinal
and Encephalic Tissue) and RED-M (Retinopathy, encephalopathy, deafness associated
microangiopathy) is a small vessel vasculitis with microinfarction due to arteriolar
occlusions. The syndrome is characterized by the triad of: encephalopathy, neurosensory
hearing loss usually bilateral and branch retinal artery occlusions.;
ICD-11 synonym : SICRET - [Small infarctions of cochlear, retinal and encephalic tissue]; Small infarctions of cochlear, retinal and encephalic tissue; Retinocochleocerebral vasculopathy; Retinopathy, encephalopathy, deafness associated microangiopathy; RED-M - [Retinopathy, encephalopathy, deafness associated microangiopathy];
ICD-11 acronym : RED-M; SICRET;
Origin ID : 1292480458;
Currated CISMeF NLP mapping
Susac syndrome, also referred to as SICRET (Small Infarctions of Cochlear, Retinal
and Encephalic Tissue) and RED-M (Retinopathy, encephalopathy, deafness associated
microangiopathy) is a small vessel vasculitis with microinfarction due to arteriolar
occlusions. The syndrome is characterized by the triad of: encephalopathy, neurosensory
hearing loss usually bilateral and branch retinal artery occlusions.
