Preferred Label : Lipodystrophy due to peptidic growth factors deficiency;
ICD-11 definition : Lipodystrophy due to peptidic growth factors deficiency is a lipodystrophic syndrome
characterized by loss of subcutaneous fat layers on the limbs, lipodystrophy in the
face and trunk and scleroderma-like skin disorders (thickened skin on the palms and
soles and skin pigment changes on the limbs and trunk).;
ICD-11 synonym : Combined insulin, insulin-like growth factor 1 (IGF1) and epidermal growth factor
(EGF) deficiency; Hoepffner-Dreyer-Reimers syndrome; Werner-like syndrome due to combined growth factor deficiency;
Origin ID : 1235390174;
Automatic exact mappings (from CISMeF team)
Lipodystrophy due to peptidic growth factors deficiency is a lipodystrophic syndrome
characterized by loss of subcutaneous fat layers on the limbs, lipodystrophy in the
face and trunk and scleroderma-like skin disorders (thickened skin on the palms and
soles and skin pigment changes on the limbs and trunk).
