Preferred Label : Kimura disease;
ICD-11 definition : Kimura disease is a chronic inflammatory disorder of poorly understood aetiology that
most commonly presents as painless lymphadenopathy or subcutaneous masses in the head
and neck region in young adults: it may cause significant disfigurement. Histologically
lymph nodes are infiltrated by dense aggregates of eosinophils, sometimes forming
eosinophilic abscesses. The disorder is associated with peripheral eosinophilia and
elevated serum IgE. It is associated with nephrotic syndrome in up to 20% of patients.;
Origin ID : 1229046951;
Automatic exact mappings (from CISMeF team)
Kimura disease is a chronic inflammatory disorder of poorly understood aetiology that
most commonly presents as painless lymphadenopathy or subcutaneous masses in the head
and neck region in young adults: it may cause significant disfigurement. Histologically
lymph nodes are infiltrated by dense aggregates of eosinophils, sometimes forming
eosinophilic abscesses. The disorder is associated with peripheral eosinophilia and
elevated serum IgE. It is associated with nephrotic syndrome in up to 20% of patients.
