Preferred Label : Organoid naevus syndrome;
ICD-11 definition : Linear nevus sebaceous syndrome (LNSS) is characterized by the association of a large
sebaceous nevus, usually appearing on the face or on the scalp, with a broad spectrum
of abnormalities that may affect every organ system, including the central nervous
system (brain neoplasms, hemimegalencephaly and lateral ventricle enlargement).;
ICD-11 synonym : Schimmelpenning-Feuerstein-Mims syndrome; Schimmelpenning syndrome; Sebaceous naevus syndrome; Linear naevus sebaceus syndrome; Solomon syndrome; Jadassohn naevus phakomatosis;
ICD-11 inclusion : Linear organoid naevus syndrome; Schimmelpenning syndrome;
Origin ID : 1218683179;
Automatic exact mappings (from CISMeF team)
Linear nevus sebaceous syndrome (LNSS) is characterized by the association of a large
sebaceous nevus, usually appearing on the face or on the scalp, with a broad spectrum
of abnormalities that may affect every organ system, including the central nervous
system (brain neoplasms, hemimegalencephaly and lateral ventricle enlargement).
