Preferred Label : Lobar holoprosencephaly;
ICD-11 definition : Lobar holoprosencephaly is the mildest classical form of holoprosencephaly (HPE) characterized
by separation of the right and left cerebral hemispheres and lateral ventricules with
some continuity across the frontal neocortex, especially rostrally and ventrally.
About 19% of HPE patients have lobar type.;
ICD-11 synonym : Lobar HPE - [holoprosencephaly]; Lobar HPE; holoprosencephaly;
Origin ID : 121649206;
Automatic exact mappings (from CISMeF team)
Lobar holoprosencephaly is the mildest classical form of holoprosencephaly (HPE) characterized
by separation of the right and left cerebral hemispheres and lateral ventricules with
some continuity across the frontal neocortex, especially rostrally and ventrally.
About 19% of HPE patients have lobar type.
