Preferred Label : Atrioventricular septal defect with communication at the atrial level only;
ICD-11 definition : A congenital cardiovascular malformation that is a variant of an atrioventricular
septal defect (atrioventricular canal defect) with an interatrial communication just
above the atrioventricular valve, no interventricular communication just below the
atrioventricular valve, separate right and left atrioventricular valvar orifices,
and varying degrees of malformation of the left sided component of the common atrioventricular
valve. The bridging leaflets of the common atrioventricular valve are bound down to
the crest of the scooped out ventricular septum so that the potential for shunting
through the atrioventricular septal defect is possible only at the atrial level and
not at the ventricular level.;
ICD-11 synonym : Partial atrioventricular canal defect; Atrioventricular defect with atrial shunting only; Partial atrioventricular canal defect with isolated atrial component; Partial atrioventricular septal defect, ostium primum type; Incomplete atrioventricular septal defect with isolated atrial component; Partial atrioventricular septal defect; Incomplete atrioventricular canal defect with isolated atrial component; Ostium primum atrial septal defect; Primum atrial septal defect;
Origin ID : 1159570489;
Automatic exact mappings (from CISMeF team)
A congenital cardiovascular malformation that is a variant of an atrioventricular
septal defect (atrioventricular canal defect) with an interatrial communication just
above the atrioventricular valve, no interventricular communication just below the
atrioventricular valve, separate right and left atrioventricular valvar orifices,
and varying degrees of malformation of the left sided component of the common atrioventricular
valve. The bridging leaflets of the common atrioventricular valve are bound down to
the crest of the scooped out ventricular septum so that the potential for shunting
through the atrioventricular septal defect is possible only at the atrial level and
not at the ventricular level.
