Preferred Label : Pigmentary retinal dystrophy;
ICD-11 definition : Retinitis pigmentosa (RP) is an inherited retinal dystrophy caused by the loss of
photoreceptors and characterized by retinal pigment deposits visible on fundus examination.
The most common form of RP is a rod-cone dystrophy, in which the first symptom is
night blindness, followed by the progressive loss in the peripheral visual field in
daylight, and eventually leading to blindness after several decades.;
Origin ID : 1142103178;
Automatic exact mappings (from CISMeF team)
Retinitis pigmentosa (RP) is an inherited retinal dystrophy caused by the loss of
photoreceptors and characterized by retinal pigment deposits visible on fundus examination.
The most common form of RP is a rod-cone dystrophy, in which the first symptom is
night blindness, followed by the progressive loss in the peripheral visual field in
daylight, and eventually leading to blindness after several decades.