Rheumatoid arthritis with splenomegaly and leukopenia

Preferred Label : Rheumatoid arthritis with splenomegaly and leukopenia;

ICD-11 definition : The triad of rheumatoid arthritis (RA), splenomegaly, and neutropenia is called Felty's syndrome. Persistent neutropenia ( 2000/mm3) must be present, but the complete triad is not required for a diagnosis of Felty's syndrome because patients without splenomegaly resemble patients with full-blown Felty's syndrome in most clinical, serologic, and immunogenetic features.;

ICD-11 synonym : rheumatoid arthritis with splenoadenomegaly and leukopenia; Felty syndrome;

ICD-11 inclusion : Large granular lymphocyte syndrome; rheumatoid arthritis with splenoadenomegaly and leukopenia;

Details

Origin ID

1118910093;

UMLS CUI

C0015773;

Currated CISMeF NLP mapping
- Felty Syndrome [NCIt concept]
- Felty syndrome [ORDO Disease]
- Felty syndrome [PASCAL descriptor]
- Felty syndrome [OMIM Phenotype]
- Felty syndrome [Disease (Nov.)]
- Felty's syndrome [DO Concept]
- Felty's syndrome [ICD-9 code]
- Felty's syndrome [ICD-10 Sub-category]
- Felty's syndrome [MedDRA Preferred Term]
- Felty's syndrome (disorder) [SNOMED CT concept]
- Feltys syndrome [ICD-10 Sub-category (who)]
- felty syndrome [MeSH concept]
- felty syndrome [MeSH Descriptor]
- felty's syndrome [SNOMED Notion]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Felty Syndrome [NCIt concept]
- Felty syndrome [OMIM Phenotype]
- Felty syndrome [Disease (Nov.)]
- Felty syndrome [ORDO Disease]
- Felty syndrome [PASCAL descriptor]
- Felty's syndrome [ICD-9 code]
- Felty's syndrome [DO Concept]
- Felty's syndrome [ICD-10 Sub-category]
- Felty's syndrome [MedDRA Preferred Term]
- Felty's syndrome (disorder) [SNOMED CT concept]
- Felty's syndrome, unspecified site [ICD-10 Subdivision]
- felty syndrome [MeSH Descriptor]
- felty syndrome [MeSH concept]
- felty's syndrome [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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