" /> Dopamine beta-hydroxylase deficiency - CISMeF





Preferred Label : Dopamine beta-hydroxylase deficiency;

ICD-11 definition : Dopamine beta-hydroxylase (DBH) deficiency is a very rare form of primary autonomic failure, and is mainly characterised by cardiovascular disorders and severe orthostatic hypotension. F;

ICD-11 synonym : Norepinephrine deficiency; Noradrenaline deficiency;

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Dopamine beta-hydroxylase (DBH) deficiency is a very rare form of primary autonomic failure, and is mainly characterised by cardiovascular disorders and severe orthostatic hypotension. F

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29/07/2025


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