Preferred Label : Medulloepithelioma;
ICD-11 definition : Medulloepitheliomas are a rare type of primitive neuroectodermal tumor of infancy
or childhood, originating from the primitive medullary epithelium in the eye and located
most often in the spinal cord and brain but occasionally in the optic nerve and manifesting
with vision loss, strabismus, proptosis and pain.;
ICD-11 inclusion : teratoid medulloepithelioma of unspecified site;
Origin ID : 1078680756;
Currated CISMeF NLP mapping
Medulloepitheliomas are a rare type of primitive neuroectodermal tumor of infancy
or childhood, originating from the primitive medullary epithelium in the eye and located
most often in the spinal cord and brain but occasionally in the optic nerve and manifesting
with vision loss, strabismus, proptosis and pain.
