Preferred Label : Fetal lower urinary tract obstruction due to posterior urethral valve;
ICD-11 definition : Congenital posterior urethral valves cause bladder obstruction in males that can manifest
along a spectrum of severity, ranging from disease incompatible with postnatal life
to conditions that have such minimal impact that they may not manifest until later
in life. Renal insufficiency is caused by PUVs in approximately 10%-15% of children
undergoing renal transplant, and approximately one third of patients born with PUVs
progress to end-stage renal disease. Moreover, as a result of the obstructive process,
increased collagen deposition and muscle hypertrophy can significantly thicken the
bladder wall. Hypertrophy and hyperplasia of the detrusor muscle and increases in
connective tissue limit bladder compliance during filling.;
ICD-11 synonym : posterior urethral valve; congenital posterior urethral valve; PUV - [posterior urethral valve];
ICD-11 acronym : PUV;
ICD-11 inclusion : congenital urethral valvular stricture; urethral valve formation; congenital urethral posterior valvular stricture; congenital valvular stricture of urethra; urethra valve; congenital urethral valve; posterior urethral valve;
Origin ID : 105479263;
Automatic exact mappings (from CISMeF team)
- See also inter- (CISMeF)
Congenital posterior urethral valves cause bladder obstruction in males that can manifest
along a spectrum of severity, ranging from disease incompatible with postnatal life
to conditions that have such minimal impact that they may not manifest until later
in life. Renal insufficiency is caused by PUVs in approximately 10%-15% of children
undergoing renal transplant, and approximately one third of patients born with PUVs
progress to end-stage renal disease. Moreover, as a result of the obstructive process,
increased collagen deposition and muscle hypertrophy can significantly thicken the
bladder wall. Hypertrophy and hyperplasia of the detrusor muscle and increases in
connective tissue limit bladder compliance during filling.
