Preferred Label : Idiopathic restrictive cardiomyopathy;
ICD-11 definition : Idiopathic restrictive cardiomyopathy is of unknown cause and also has distinct morphologic
and haemodynamic characteristics that separate it from dilated and hypertrophic cardiomyopathy.
The characteristics consist of a non-dilated ventricle with typically normal wall
thickness, ventricular walls that are rigid, resulting in severe diastolic dysfunction
and restrictive filling pattern with elevated filling pressures and dilated atria,
and generally normal left ventricular systolic function.;
ICD-11 synonym : Primary restrictive cardiomyopathy;
Origin ID : 1034845657;
Automatic exact mappings (from CISMeF team)
Idiopathic restrictive cardiomyopathy is of unknown cause and also has distinct morphologic
and haemodynamic characteristics that separate it from dilated and hypertrophic cardiomyopathy.
The characteristics consist of a non-dilated ventricle with typically normal wall
thickness, ventricular walls that are rigid, resulting in severe diastolic dysfunction
and restrictive filling pattern with elevated filling pressures and dilated atria,
and generally normal left ventricular systolic function.
