Preferred Label : Legius syndrome;
ICD-11 definition : Legius syndrome, also known as neurofibromatosis type 11-like syndrome, is a very
rare, genetic, skin pigmentation disorder characterized by multiple café-au-lait macules
with or without axillary or inguinal freckling.;
ICD-11 synonym : NF1-like syndrome; Neurofibromatosis 1-like syndrome; NFLS - [Neurofibromatosis 1-like syndrome] (MIM 611431); NFLS - [Neurofibromatosis 1-like syndrome];
ICD-11 acronym : NFLS;
Origin ID : 1025118245;
Automatic exact mappings (from CISMeF team)
Legius syndrome, also known as neurofibromatosis type 11-like syndrome, is a very
rare, genetic, skin pigmentation disorder characterized by multiple café-au-lait macules
with or without axillary or inguinal freckling.
