Preferred Label : Catel-Manzke syndrome;
ICD-11 definition : Catel-Manzke syndrome is a rare association combining micrognathia, glossoptosis and
cleft palate (Pierre Robin sequence) with an anomaly of both index fingers (accessory
ossicle at the metacarpophalangeal joint with resulting ulnar deviation).;
Origin ID : 1023183031;
Automatic exact mappings (from CISMeF team)
Catel-Manzke syndrome is a rare association combining micrognathia, glossoptosis and
cleft palate (Pierre Robin sequence) with an anomaly of both index fingers (accessory
ossicle at the metacarpophalangeal joint with resulting ulnar deviation).