Preferred Label : Hashimoto-Pritzker syndrome;
ICD-11 definition : Hashimoto-Pritzker histiocytosis (HPH) is a variant of Langerhans cell histiocytosis
characterized by multiple disseminated skin lesions (firm, red-brown, painless papulo-nodules).;
Origin ID : 1011705244;
Automatic exact mappings (from CISMeF team)
Hashimoto-Pritzker histiocytosis (HPH) is a variant of Langerhans cell histiocytosis
characterized by multiple disseminated skin lesions (firm, red-brown, painless papulo-nodules).