ICD-11 code : XH6PA4;
Preferred Label : Kaposiform haemangioendothelioma;
ICD-11 definition : Kaposiform haemangioendothelioma is a rare low-grade malignant cutaneous or visceral
vascular tumour that may be associated with severe thrombopaenia with consumption
coagulopathy (Kasabach-Merritt syndrome) in paediatric patients.;
Origin ID : 248477855;
Automatic exact mappings (from CISMeF team)
Kaposiform haemangioendothelioma is a rare low-grade malignant cutaneous or visceral
vascular tumour that may be associated with severe thrombopaenia with consumption
coagulopathy (Kasabach-Merritt syndrome) in paediatric patients.
