ICD-11 definition : Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast
cells infiltrate the entire skin diffusely. It usually presents in the neonatal period
and is characterized by erythroderma, a doughy ''peau d'orange'' appearance and blistering
after minor trauma. Affected infants are at risk of systemic disease and severe complications
including anaphylaxis and diarrhoea. The condition may resolve spontaneously.;
Diffuse cutaneous mastocytosis is a rare form of cutaneous mastocytosis in which mast
cells infiltrate the entire skin diffusely. It usually presents in the neonatal period
and is characterized by erythroderma, a doughy ''peau d'orange'' appearance and blistering
after minor trauma. Affected infants are at risk of systemic disease and severe complications
including anaphylaxis and diarrhoea. The condition may resolve spontaneously.
Currated CISMeF NLP mapping